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Pathology
Affects small to medium sized vessels.
Necrotising granuloma affecting vessels of lungs, GI tract and peripheral nerves
Aetiology
Associated with pANCA
Signs
3 distinct stages
1. Sinusitis and onset of allergies
2. Onset of acute asthma
3. Systemic involvement: skin purpura, GI upset, peripheral neuropathy.
Symptoms
Chest tightness, wheeze, Shortness of breath, sinusitis
Investigations
Bloods: FBC shows eosinophilia, pANCA, CRP and ESR
Imaging: Chest X-ray shows eosinophilic lung deposits.Treatment
Medical: Steroids, immunosuppression
Prognosis
Poor prognosis and end organ damage
Glomerulonephritis, vasculitis
Key Facts
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Key Images
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Key References
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