Reading Time:

Pathology

Low or abnormal vWF resulting in low levels of factor VIII and disorders of platelet function

Aetiology

Autosomal dominant inheritance 

Signs

Intermittent mucocutaneous bleeding

Symptoms

Menorrhagia, Epistaxis

Investigations

Clotting screen:  Prolonged APTT, normal PT,  Low vWF levels and function. 
Normal Factor VIII, Increased bleeding time

Treatment

Medical: Desmopressin (can increase vWF levels), vWF rich factor VIII
vWF concentrate, Tranexamic acid, fresh frozen plasma

Prognosis

Usually very good
Excessive bleeding 

Key Facts

Lorem ipsum dolor sit amet, sapien platea morbi dolor lacus nunc, nunc ullamcorper. Felis aliquet egestas vitae, nibh ante quis quis dolor sed mauris.

Key Images

Lorem ipsum dolor sit amet, sapien platea morbi dolor lacus nunc, nunc ullamcorper. Felis aliquet egestas vitae, nibh ante quis quis dolor sed mauris.

Key References

Lorem ipsum dolor sit amet, sapien platea morbi dolor lacus nunc, nunc ullamcorper. Felis aliquet egestas vitae, nibh ante quis quis dolor sed mauris.